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Chronic neurogenic quadriceps amyotrophy
Author(s) -
Furukawa Tetsuo,
Akagami Noriko,
Maruyama Shoichi
Publication year - 1977
Publication title -
annals of neurology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 4.764
H-Index - 296
eISSN - 1531-8249
pISSN - 0364-5134
DOI - 10.1002/ana.410020614
Subject(s) - medicine , amyotrophy , wasting , weakness , atrophy , muscle biopsy , biopsy , surgery
Two patients with chronic neurogenic quadriceps amyotrophy are reported. A 61‐year‐old woman had symmetrical wasting and weakness of the quadriceps femoris of eight years' duration. A biopsy revealed neuropathic changes, and electromyograms showed neurogenic as well as myopathic patterns in the quadriceps and other muscles. A 29‐year‐old woman had long‐standing wasting limited to the quadriceps and hip muscles. EMG and biopsy were compatible with neurogenic atrophy. She had a brother suffereing from a more widespread and severe form of the disease. These cases suggest that chronic neurogenic quadriceps amyotrophy is a forme fruste of Kugelberg‐Welander disease.