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Sickle hemoglobinopathies in sicily
Author(s) -
Schilirò G.,
Spena M.,
Giambelluca E.,
Maggio A.
Publication year - 1990
Publication title -
american journal of hematology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.456
H-Index - 105
eISSN - 1096-8652
pISSN - 0361-8609
DOI - 10.1002/ajh.2830330202
Subject(s) - beta thalassemia , beta (programming language) , medicine , hemoglobinopathy , disease , sicilian , beta thalassaemia , pediatrics , gastroenterology , thalassemia , philosophy , linguistics , computer science , programming language
The clinical and hematological features of 202 Sicilian subjects with sickle cell disease are reported, 41 being homozygous for beta S (β S β S ), 64 with beta s thal beta S (β s β S ), and 97 beta + thal beta S (β + β S ). Analysis of the findings showed that the disease observed in Sicilians is of intermediate severity and falls between the severe form observed in patients of African origin and the milder one seen in subjects of Arabian origin.