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Intracranial extramedullary hematopoiesis in β°‐thalassemia/hemoglobin E disease
Author(s) -
Fucharoen Suthat,
Tunthanavatana Chalermchai,
Sonakul Dhira,
Wasi Prawase
Publication year - 1981
Publication title -
american journal of hematology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.456
H-Index - 105
eISSN - 1096-8652
pISSN - 0361-8609
DOI - 10.1002/ajh.2830100111
Subject(s) - thalassemia , extramedullary hematopoiesis , medicine , pseudotumor cerebri , hematologic disease , hemoglobin , atrophy , pathology , intracranial pressure , disease , haematopoiesis , radiology , biology , stem cell , genetics
A 27‐year‐old woman with β‐thalassemia/hemoglobin E disease presented with an intracranial mass of 10 × 9 × 1.2 cm firmly attached to the dura and the falx cerebri extending over the central part of both hemispheres, with pressure atrophy of the underlying brain. Histopathologic examination revealed that the mass consisted entirely of hematopoietic cells. We have seen 1,315 cases with β‐thalassemia/hemoglobin E, but this was the first case with intracranial extramedullary hematopoietic mass.