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Type la glycogenosis associated with hepatocellular carcinoma
Author(s) -
Conti John A.,
Kemeny Nancy
Publication year - 1992
Publication title -
cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.052
H-Index - 304
eISSN - 1097-0142
pISSN - 0008-543X
DOI - 10.1002/1097-0142(19920315)69:6<1320::aid-cncr2820690603>3.0.co;2-d
Subject(s) - hepatocellular carcinoma , medicine , glycogen storage disease type i , carcinoma , neoplasm , liver disease , disease , gastroenterology , glycogen storage disease , pathology
The predispostion of preexisting cirrhotic metabolic liver disease to the development of hepatocellular carcinoma is well established. However, the association between glycogenoses (a form of noncirrhotic metabolic liver disease) and the formation of benign and malignant liver tumors is less well known. The sixth case of simultaneous occurrence of glycogenosis type la and hepatocellular carcinoma, which occurred in a 34‐year‐old man referred for advice on therapy for his malignant neoplasm, is reported. Cases previously described in the literature are reviewed and management of this entity in light of the current knowledge in the diagnosis and treatment of hepatocellular carcinoma is discussed. Cancer 1992; 69:1320‐1322.