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Primary peripheral neuroepithelioma of the orbit with intracranial extension
Author(s) -
Wilson W. Bruce,
Roloff James,
Wilson Harry L.
Publication year - 1988
Publication title -
cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.052
H-Index - 304
eISSN - 1097-0142
pISSN - 0008-543X
DOI - 10.1002/1097-0142(19881215)62:12<2595::aid-cncr2820621224>3.0.co;2-y
Subject(s) - medicine , orbit (dynamics) , radiation therapy , edema , peripheral , chemotherapy , peripheral edema , radiology , sarcoma , surgery , pathology , adverse effect , engineering , aerospace engineering
A 7‐year‐old girl with clinical signs limited to moderate unilateral proptosis of 2 weeks duration and ipsilateral disc edema was found to have a contiguous orbital and subfrontal intracranial tumor best characterized as a peripheral neuroepithelioma by recent studies. Previously this tumor would have been called an extraosseous Ewing's sarcoma. The tumor had a significant lobular component on either side of the orbital roof. The patient is still alive 24 months posttreatment with multimodal excisional surgery, radiation, and chemotherapy.