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Bone sarcomas associated with ollier's disease
Author(s) -
Liu Jue,
Hudkins Philip G.,
Swee Ronald G.,
Unni Krishnan K.
Publication year - 1987
Publication title -
cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.052
H-Index - 304
eISSN - 1097-0142
pISSN - 0008-543X
DOI - 10.1002/1097-0142(19870401)59:7<1376::aid-cncr2820590725>3.0.co;2-f
Subject(s) - medicine , chondrosarcoma , osteosarcoma , sarcoma , chordoma , appendicular skeleton , disease , bone sarcoma , pathology , anatomy
Of 55 patients with Ollier's disease seen at the Mayo Clinic between 1907 and 1985, 16 had malignant bone neoplasms: 12 chondrosarcomas, two dedifferentiated chondrosarcomas, one chordoma, and one osteosarcoma. One patient had a chondrosarcoma in two different bones. These findings suggest that approximately 30% of patients with Ollier's disease will develop a malignant bone neoplasm, most probably chondrosarcoma. The prognosis for most patients is good. Five of the 16 patients survived more than 13 years after treatment.