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Lymphangiomyomatosis with chylous ascites. Treatment with dietary fat restriction and medium chain triglycerides
Author(s) -
Calabrese Patrick R.,
Frank H. David,
Taubin Howard L.
Publication year - 1977
Publication title -
cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.052
H-Index - 304
eISSN - 1097-0142
pISSN - 0008-543X
DOI - 10.1002/1097-0142(197708)40:2<895::aid-cncr2820400245>3.0.co;2-8
Subject(s) - chylous ascites , medicine , chyle , lymph , ascites , lymphatic system , chemotherapy , gastroenterology , pleural effusion , surgery , pathology , complication
Lymphangiomyomyoma is a tumor of lymphatic channels and lymph nodes, clinically manifested by recurrent chylous pleural effusions and ascites. The disease is usually progressive and unresponsive to surgery, chemotherapy, or irradiation. A case of lymphangiomyomatosis in a 24‐year‐old woman who presented with chylous ascites is described. The patient was treated with dietary fat restriction supplemented with medium chain triglycerides and has remained free of recurrent effusions for 2 years. Cancer 40:895–897, 1977.