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Rhabdomyosarcoma of lung arising in congenital cystic adenomatoid malformation
Author(s) -
Ueda Kazuhiro,
Gruppo Ralph,
Unger Frances,
Martin Lester,
Bove Kevin
Publication year - 1977
Publication title -
cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.052
H-Index - 304
eISSN - 1097-0142
pISSN - 0008-543X
DOI - 10.1002/1097-0142(197707)40:1<383::aid-cncr2820400154>3.0.co;2-2
Subject(s) - medicine , congenital cystic adenomatoid malformation , asymptomatic , rhabdomyosarcoma , embryonal rhabdomyosarcoma , lung , surgery , sarcoma , pathology , pregnancy , fetus , genetics , biology
An asymptomatic congenital cystic adenomatoid malformation of lung discovered at age 18 months, and unchanging for 14 months prior to its removal, was found to harbor a small embryonal rhabdomyosarcoma following excision. With lobectomy and chemotherapy, the tumor‐free interval has now exceeded three years. The case represents a well‐documented occurrence of malignant tumor arising within a congenital malformation, an association that is unlikely to be the result of chance. Cancer 40:383–388, 1977.