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Congenital hepatic fibrosis, liver cell carcinoma and adult polycystic kidneys
Author(s) -
Manes Jose L.,
Kissane John M.,
Valdes Andres J.
Publication year - 1977
Publication title -
cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.052
H-Index - 304
eISSN - 1097-0142
pISSN - 0008-543X
DOI - 10.1002/1097-0142(197706)39:6<2619::aid-cncr2820390647>3.0.co;2-4
Subject(s) - medicine , congenital hepatic fibrosis , pathology , hyaline , muscle hypertrophy , fibrosis , carcinoma , polycystic kidney , esophagus , stomach , cyst , portal hypertension , cirrhosis
In reviewing the literature, we found no liver cell carcinoma (LCC) or well‐documented adult polycystic kidneys (APK) associated with congenital hepatic fibrosis (CHF). We report a 69‐year‐old man with CHF, LCC, APK, duplication cyst of distal portion of stomach, two calcified splenic artery aneurysms, myo‐cardial fibrosis and muscular hypertrophy of esophagus. The LCC was grossly pedunculated and microscopically showed prominent fibrosis and hyaline intracytoplasmic inclusions in the tumor cells.