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Cherubism: An analysis of treatment
Author(s) -
Hamner James E.,
Ketcham Alfred S.
Publication year - 1969
Publication title -
cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.052
H-Index - 304
eISSN - 1097-0142
pISSN - 0008-543X
DOI - 10.1002/1097-0142(196905)23:5<1133::aid-cncr2820230519>3.0.co;2-q
Subject(s) - cherubism , medicine , masticatory force , dentistry , surgery , giant cell , pathology
The surgical treatment and 5‐year follow‐up for two siblings suffering with cherubism is presented along with a brief resumé of possible treatment courses. The girl first demonstrated bilateral mandibular swellings at age 14 months, which makes her the youngest reported child with cherubism's clinical manifestation. Curettement was the treatment of choice for both children. Untreated jaw lesions did not show regression, but rather progressed in a fashion similar to tumor that was left behind in some of the recontoured areas. Progression continued from age 14 months to 8 years. Multilocular tumor rarefactions were found to remain in both jaws of each child after 5 years. Two maxillary facial and one mandibular curettements were required for the sister. Her brother's maxillary lesions were curetted once, and his mandibular lesions were curetted twice. The cosmetic results for both children were satisfactory, and as many permanent teeth as possible were spared for future masticatory function. One can only conclude that each child suffering from cherubism must be evaluated individually, considering his family history, his age, the rate of tumor progression, and extent of tumor involvement before judging what degree of surgical management is required for that particular patient to obtain the best cosmetic and future masticatory results.