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Multiple mucosal neuromas, pheochromocytoma and medullary carcinoma of the thyroid—a syndrome
Author(s) -
Gorlin Robert J.,
Sedano Heddie O.,
Vickers Robert A.,
Červenka Jaroslav
Publication year - 1968
Publication title -
cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.052
H-Index - 304
eISSN - 1097-0142
pISSN - 0008-543X
DOI - 10.1002/1097-0142(196808)22:2<293::aid-cncr2820220206>3.0.co;2-r
Subject(s) - medicine , cornea , diverticulosis , pheochromocytoma , medullary carcinoma , medullary cavity , pathology , thyroid , neuroma , conjunctiva , thyroid carcinoma , anatomy , surgery , ophthalmology
An analysis of 17 cases of the syndrome of multiple mucosal neuromas, pheochromocytoma and medullary carcinoma of the thyroid is presented and its relationship to similar syndromes discussed. The mucosal neuromas primarily involve the lips, anterior tongue, conjunctiva and nasal and laryngeal mucosa. Medullated corneal nerve fibers traverse the cornea and anastomose in the pupillary area. A Marfanoid build and diverticulosis may be associated findings.