Premium
Rare pulmonary manifestations of tuberous sclerosis in children
Author(s) -
Bowen John,
Beasley Spencer W.
Publication year - 1997
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/(sici)1099-0496(199702)23:2<114::aid-ppul6>3.0.co;2-p
Subject(s) - tuberous sclerosis , medicine , pneumothorax , lung , pathology , dermatology , pediatrics , surgery
Tuberous sclerosis is one of the rare neurocutaneous syndromes and may involve organs other than skin and brain. Pulmonary involvement is uncommon and predominantly affects women of childbearing age. Those affected present with dyspnea or spontaneous pneumothorax from cystic or fibrous degeneration of the lung. Males are affected very rarely. This paper describes another manifestation of pulmonary involvement in tuberous sclerosis, namely, recurrent intrapleural cysts in a young boy. Pediatr. Pulmonol. 1997; 23:114–116. © 1997 Wiley‐Liss, Inc.