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Chronic demyelinating hypertrophic brachial plexus neuropathy
Author(s) -
van den Bergh Peter Y.K.,
Thonnard JeanLouis,
Duprez Thierry,
Laterre E. Christian
Publication year - 2000
Publication title -
muscle and nerve
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.025
H-Index - 145
eISSN - 1097-4598
pISSN - 0148-639X
DOI - 10.1002/(sici)1097-4598(200002)23:2<283::aid-mus23>3.0.co;2-q
Subject(s) - medicine , multifocal motor neuropathy , polyradiculoneuropathy , brachial plexus , muscle hypertrophy , magnetic resonance imaging , anesthesia , guillain barre syndrome , mismatch negativity , radiology , electroencephalography , psychiatry , immunology
A patient with unilateral, painless, chronic progressive upper limb sensorimotor deficit showed electrophysiological evidence of a focal demyelinating neuropathy with almost complete conduction block across the brachial plexus. Magnetic resonance imaging disclosed marked brachial plexus hypertrophy. Intravenous immunoglobulin led to fast and complete recovery, maintained by intermittent perfusions. Hypertrophic brachial plexus neuropathy can be a presentation of focal chronic inflammatory demyelinating polyradiculoneuropathy. Objective and quantitative assessment of hand function is useful to evaluate treatment results and to optimize treatment regimens. © 2000 John Wiley & Sons, Inc. Muscle Nerve 23: 283–288, 2000.