Progressive Hemifacial Atrophy With Contralateral Uveitis: A Case Report
Author(s) -
Önder Ayyıldız,
Simel Ayyıldız,
Ali Hakan Durukan,
Güngör Sobacı
Publication year - 2015
Publication title -
iranian red crescent medical journal
Language(s) - English
Resource type - Journals
eISSN - 2074-1812
pISSN - 2074-1804
DOI - 10.5812/ircmj.16168
Subject(s) - medicine , enophthalmos , atrophy , dermatology , surgery , retinal vasculitis , uveitis , vasculitis , ophthalmology , pathology , disease , diplopia
Progressive hemifacial atrophy, known as Parry-Romberg syndrome (PRS), was first described by Parry in 1825. There is a progressive atrophy of facial tissues including skin, bones and muscles. Ophthalmic disorders are common and include keratitis, uveitis, cataract, ipsilateral enophthalmos, optic neuritis, retinal vasculitis and scleral melting.We describe a patient with progressive hemifacial atrophy at right facial side who developed granulomatous uveitis and periferic retinal vasculitis in his left eye. We started topical and systemic steroid therapy. Uveitic reaction had regressed almost entirely after a 3-month steroid treatment.The individuals should have multidisciplinary approach for the variety of disorders to maintain the appropriate treatment for a better appearance of the patients.
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