Anesthetic Management in a Child With Niemann-Pick Disease | Zendy

Ebrahim Espahbodi | Zendy; Amir Abbas Yaghooti | Zendy; Abbas Ostadalipour | Zendy; Shaqayeq Marashi | Zendy

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Anesthetic Management in a Child With Niemann-Pick Disease

Author(s) -

Ebrahim Espahbodi,

Amir Abbas Yaghooti,

Abbas Ostadalipour,

Shaqayeq Marashi

Publication year - 2016

Publication title -

iranian journal of pediatrics

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 0.168

H-Index - 25

eISSN - 2008-2150

pISSN - 2008-2142

DOI - 10.5812/ijp.5479

Subject(s) - medicine , niemann–pick disease , anesthetic , disease , intensive care medicine , lysosomal storage disease , pediatrics , anesthesia

Niemann-Pick is a lipid storage disease that results from a lysosomal enzyme deficiency (sphingomyelinase). It has different presentations, and it may affect various organs such as the central nervous system, kidney, liver, and spleen. Due to the complexity of the disease, careful perianesthetic management is necessary in order to reduce the risks and sequels. As there is little evidence available in the literature regarding the anesthetic implications of such patients, in this case report we describe the anesthetic management of a two-year-old female with Niemann-Pick disease.

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