Clear Cell Odontogenic Carcinoma Of The Maxilla: A Case Report

Clear cell odontogenic carcinoma (CCOC) is a rare odontogenic tumor that tends to occur in the mandible of older adults with a predilection for women. We describe a case which occurred in the maxilla and metastasized to the cervical regional lymph nodes of a 45 year old female Nigerian. This article highlights the clinico-pathologic features of CCOC that were confirmed by histopathological examination of the case. Other secondary or primary sites of the lesion were excluded by clinical and radiological examinations. Special staining for mucin ruled out a salivary gland tumor. The aggressive potential of this neoplasm is well documented and resection with negative margins is the treatment of choice. In view of the notable number of cases with metastasis, elective neck dissection and adjuvant radiotherapy should be considered as part of the treatment modality. The present report is an addition to the sparse literature.