Portohepatic shunt in a patient without cirrhosis

Background: A 65-year-old woman was admitted with complaint of a left gluteal mass. She had a history of congenital hip dislocation and a known splenic enlargement for more than 40 years. The patient had pancytopenia on admission. Hematocrit level 23.7%, white blood cell count 2.5 x 103/uL, platelet count 69 x 103/uL were measured. Liver function tests were normal. Viral markers such as hepatitis B surface antigen and anti-hepatitis C related to liver disease were negative. There was no known liver biopsy or history of trauma.