Sturge-Weber Syndrome Type III

The classical triad of Sturge-Weber syndrome is a port-wine stain on the face, glaucoma and leptomeningeal angiomas. While Type I might include the whole triad, Type II presents with the involvement of the skin without leptomeningeal angiomas. Type III Sturge-Weber syndrome is the rarest subtype and presents with leptomeningeal involvement without the port-wine stain on the face (1-3). Only a few cases of this type have been reported, and its incidence is unknown (4-7). This subtype is generally diagnosed based on the findings of leptomeningeal angiomas in contrast brain magnetic resonance imaging (MRI) scans and calcifications in the same region via brain computed tomography (CT) scans of patients presenting with seizures (4,5). Here, we present the case of a 5.5-month-old patient with Type III SturgeWeber syndrome presenting with seizures. Case Report