Marfan syndrome | Zendy

T Sivasankari | Zendy; Philips Mathew | Zendy; RaviDavid Austin | Zendy; Sakthi Devi | Zendy

AI Assistant Blog Pricing

Home ZAIA Blog

Open Access

Marfan syndrome

Author(s) -

T Sivasankari,

Philips Mathew,

RaviDavid Austin,

Sakthi Devi

Publication year - 2017

Publication title -

journal of pharmacy and bioallied sciences

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 0.268

H-Index - 36

eISSN - 0976-4879

pISSN - 0975-7406

DOI - 10.4103/jpbs.jpbs_326_16

Subject(s) - medicine , hypodontia , connective tissue , connective tissue disorder , scoliosis , dentistry , surgery , pathology

Marfan syndrome (MFS) is the autosomal dominant-inherited multisystem connective-tissue disorder, with a reported incidence of 1 in 10,000 individuals and equal distribution in both genders. The main clinical manifestation of this disorder consists of an exaggerated length of the upper and lower limbs, hyperlaxity, scoliosis, alterations in the cardiovascular and pulmonary systems, and atypical bone overgrowth. Orofacial manifestations such as high-arched palate, hypodontia, long narrow teeth, bifid uvula, mandibular prognathism, and temporomandibular disorders are also common. Early diagnosis of MFS is essential to prevent the cardiovascular complications and treatment of orofacial manifestations, thus to increase the quality of life of the patient.

The content you want is available to Zendy users.

Already have an account? Click here to sign in.

Having issues? You can contact us here

Accelerating Research