Proteus syndrome: a case report and a case study review in China | Zendy

Xibao Zhang | Zendy; Changxing Li | Zendy; Yuqing He | Zendy; Sanquan Zhang | Zendy; Yan-Xia Cai | Zendy

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Proteus syndrome: a case report and a case study review in China

Author(s) -

Xibao Zhang,

Changxing Li,

Yuqing He,

Sanquan Zhang,

Yan-Xia Cai

Publication year - 2010

Publication title -

dermatology reports

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 0.183

H-Index - 10

eISSN - 2036-7406

pISSN - 2036-7392

DOI - 10.4081/dr.2010.e3

Subject(s) - proteus syndrome , medicine , hyperostosis , natural history , connective tissue , pathology , dermatology , anatomy

Proteus syndrome (PS) is a rare and sporadic disorder characterized by overgrowth of multiple tissues and a propensity to develop particular neoplasms. The clinical manifestations of PS include macrodactyly, vertebral abnormalities, asymmetric limb overgrowth and length discrepancy, hyperostosis, abnormal and asymmetric fat distribution, asymmetric muscle development, connective tissue nevi, and vascular malformations. We report a 16-year old female patient who manifested a number of these complications and review the Chinese literature about the diagnosis, natural history, and management of PS

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