Poland syndrome associated with contralateral gynecomastia

Poland syndrome is an uncommon congenital birth defect that may present with partial or complete absence of the pectoralis muscle. It is commonly accompanied by nipple-areolar complex, breast abnormalities, thinning of subcutaneous tissue, deformities of ribs, axillary and pectoral hair absence, and unilateral hand syndactyly. Some of these anomalies present at puberty. Out of these, the chest may become more apparent. However, severely affected children could have these anomalies in hand or chest from birth.