Endovascular embolization of ruptured giant pseudoaneurysm of renal angiomyolipoma in a patient with tuberous sclerosis

Tuberous sclerosis (TS) is a neuro-cutaneous disorder characterized by the development of multiple benign tumours. Renal angiomyolipoma (AML) is a benign tumour associated with 55-80% of patients with TS complex [1]. Typical histology reveals triphasic tumour with myoid spindle cells, mature adipose tissue and dysmorphic thick-walled blood vessels without elastic lamina [3]. Radiologically, it is characterized by the fat content. It is associated with arterial pseudoaneurysm which can lead to life threatening complications. We present a case of ruptured giant pseudoaneurysm with intra capsular hematoma in a renal angiomyolipoma associated with TS.