Neurocutaneous melanoma in association with giant congenital melanocytic nevi in a child (Touraine syndrome) – A dermatoradiological correlation | Zendy

Juvaina Puthiyakam | Zendy; Najeeba Riyaz | Zendy; Faiz Riyaz Arakkal | Zendy; Riyaz Arakkal | Zendy

Open Access

Neurocutaneous melanoma in association with giant congenital melanocytic nevi in a child (Touraine syndrome) – A dermatoradiological correlation

Author(s) -

Juvaina Puthiyakam,

Najeeba Riyaz,

Faiz Riyaz Arakkal,

Riyaz Arakkal

Publication year - 2020

Publication title -

journal of skin and sexually transmitted diseases

Language(s) - English

Resource type - Journals

eISSN - 2994-6026

pISSN - 2582-3175

DOI - 10.25259/jsstd_36_2020

Subject(s) - congenital melanocytic nevus , medicine , melanoma , leptomeninges , dermatology , melanosis , trunk , pathology , nevus , melanocytic nevus , superficial spreading melanoma , central nervous system , biology , ecology , cancer research

Touraine syndrome or neurocutaneous melanosis/melanoma is a rare melanophakomatosis characterized by extensive/multiple congenital melanocytic nevi associated with cerebral/meningeal melanosis or melanoma. We report a 12-year-old boy with a congenital giant melanocytic nevus on the bathing trunk distribution with scattered lesions on the face, neck, and legs. MRI brain revealed a melanoma in the right amygdala.

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