Ebstein Anomalisinde Carpentier Tipi Kapak Tamiri / Carpentier Type Valve Reconstruction in Ebstein’s Anomaly

Oz: Ebstein anomalisinde trikuspid kapagin apikal yerdegistirme miktari ve sag ventrikulun hipoplazisinin agirligina bagli olarak tek ventrikul, 1+½ ventrikul veya cift ventrikul tamirleri uygulanabilmektedir. 1+½ ventrikul veya cift ventrikul tamirleri dahilinde trikuspid kapaga pekcok farkli rekonstruksiyon proseduru uygulanmaktadir. Bu prosedurler arasinda Carpentier tipi trikuspid kapak rekonstruksiyonunun mortalite, morbidite ve reoperasyon oranlarinin dusuk oldugu bildirilmektedir. Bu calismada, Tip 2 Ebstein anomalisine sahip eriskin bir hastada Carpentier tipi trikuspid kapak rekonstruksiyonu ile birlikte basarili 1+½ ventrikul tamiri sunulmaktadir. Anahtar Kelimeler: Ebstein anomalisi, trikuspid kapak tamiri, Carpentier tipi kapak tamiri, tek ventrikul, 1+½ ventrikul Abstract: Single ventricle, 1+½ ventricle or double ventricle repairs may be performed in patients with Ebstein’s anomaly depending on the severity of the right ventricular hypoplasia and extent of the apical displacement of the tricuspid valve. Several reconstruction procedures are used to be performed for the repair of tricuspid valve within 1+½ ventricle and double ventricle repairs. Among these procedures, Carpentier type tricuspid valve reconstruction was reported with low mortality, morbidity and reoperation rates. In this study, successful 1+½ ventricle repair using Carpentier type tricuspid valve reconstruction is presented in an adult patient with Type 2 Ebstein’s anomaly. Keywords: Ebstein’s anomaly, tricuspid valve repair, Carpentier type valve repair, single ventricle, 1+½ ventricle