Ebstein’s anomaly and Left Ventricular Non Compaction Cardiomyopathy: a Not So Unusual Association
Author(s) -
Daniele Andreini,
Gianluca Pontone,
Saima Mushtaq,
Emanuela Muratori,
Marco Guglielmo,
Edoardo Conte,
P. Carita',
Mauro Pepi
Publication year - 2016
Publication title -
international cardiovascular forum journal
Language(s) - English
Resource type - Journals
eISSN - 2410-2636
pISSN - 2409-3424
DOI - 10.17987/icfj.v8i0.288
Subject(s) - life span , cardiomyopathy , span (engineering) , medicine , cardiology , ebstein's anomaly , ventricle , heart failure , gerontology , civil engineering , engineering
Left ventricular n on-compaction (LVNC) is a rare congenital cardiomyopathy. It is thought to be a congenital arrest of endomyocardial embryogenesis in utero . It has been reported the association with other cardiac abnormalities. We pre sented two cases of association of LVNC and Ebstein's anomaly. The cardiac magnetic resonance (CMR) allows a comprehensive evaluation of associated findings. All patients with Ebstein’s anomaly should be carefully evaluated for LVNC. The prompt identification of myocardial non compaction is important because of its high mortality due to progressive heart failure, tromboembolism and malignant arrhythmias
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