HURLER SENDROMU’NUN (MUKOPOLİSAKKARİDOZ-I) ORAL BULGULARI: OLGU SUNUMU

Hurler syndrome (Mucopolysaccharidosis type I) is one of the genetic disorders involving disturbances in mucopolysaccharide metabolism resulting in increased storage of acid mucopolysaccharide in various tissues. An 7-year-old girl with Hurler syndrome is described in this article, with special emphasis on the oral, dental and radiographic findings. Key Mucopolysaccharidosis type I, oral finding, dentistywords: Hurler syndrome