Bilateral facial and cervical port-wine stain and Sturge-Weber syndrome

Sturge-Weber syndrome is a rare phakomatosis syndrome. One of the cardinal features of that syndrome is the facial port-wine stain (nevus flammeus). The stain is usually seen within the distribution of the ophthalmic branch of the trigeminal nerve on one side. Extensive and bilateral facial as well as extra-facial (neck) involvement are rare and increase the likelihood of the diagnosis of Sturge-Weber syndrome.