Open AccessRespiratory Management of Myotonic Dystrophy
Author(s) -
Bach John R,
Chiarello Giulio,
Gonapa Somnath
Publication year - 2020
Publication title -
archives of pulmonology and respiratory care
Language(s) - English
Resource type - Journals
ISSN - 2581-3684
DOI - 10.17352/aprc.000043
Subject(s) - myotonic dystrophy , medicine , respiratory failure , pediatrics , sleep (system call) , anesthesia , hypercapnia , respiratory system , computer science , operating system
Patients with myotonic dystrophy can avoid episodes of respiratory failure by using up to continuous noninvasive ventilatory support (CNVS). Of 154 patients consecutively presenting to a neuromuscular disease clinic, 143 had types 1 or 2 and 11 had congenital myotonic dystrophy. Of the 76 who came multiple times, 41 were prescribed and used at least sleep NVS to relieve symptoms of fatigue and hypersomnolence.
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