Dyke-Davidoff-Masson Syndrome: A case report.

Dyke-Davidoff-Masson Syndrome (DDMS) refers to atrophy or hypoplasia of one cerebral hemisphere (hemi atrophy) which is secondary to brain insult in fetal or early childhood period. Hemi atrophy is not frequently encountered in clinical practice. This clinical condition manifests with seizures, facial asymmetry, contra lateral spastic hemiplegia or hemiparesis and rarely mental retardation. The characteristic radiologic features are cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. We report here a case of a 6 year old boy with features suggestive of DDMS.