Bilateral nephron-sparing surgery for giant bilateral renal angiomyolipomas associated with tuberous sclerosis complex Dev bilateral renal anjiyomyolipom ve tuberosklerozis kompleksli hastada bilat

R enal angiomyolipoma is a rare benign neoplasm (1-3% of all renal tumors) composed of varying amounts of mature adipose tissue, smooth muscle and thick-walled blood vessels. A 20% of all renal AMLs are associated with tuberous sclerosis. In patients with TSC, AML is usually multiple, bilateral and symptomatic natures. Patient’s symptoms and size of the lesion are the determinants for the choice of the treatment. In general, symptomatic or greater than 8 cm masses require intervention. Due to its benign nature, renal AMLs represents an ideal lesion for nephronsparing treatment by tumour enucleation, partial nephrectomy or selective arterial embolization (1,2). However, there are limited numbers data with regard to nephron sparing surgery of renal AMLs especially in bilateral cases with TSC. We report the treatment result of bilateral nephron-sparing surgery of a patient with giant bilateral renal AMLs and TSC.