Adult-Onset Still's Disease and Cardiac Tamponade: A Rare Association
Author(s) -
Pedro CarrilhoFerreira,
Doroteia Silva,
Maria de Jesus Silva,
Rui André,
Manuel Varela,
António Nunes Diogo
Publication year - 2015
Publication title -
texas heart institute journal
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.373
H-Index - 53
eISSN - 1526-6702
pISSN - 0730-2347
DOI - 10.14503/thij-14-4101
Subject(s) - medicine , cardiac tamponade , pericardial effusion , pericarditis , tamponade , differential diagnosis , disease , rare disease , sequela , surgery , pericardiectomy , cardiac surgery , cardiology , pathology
Adult-onset Still's disease is a rare disorder with potentially severe clinical features, including cardiac involvement. This systemic inflammatory disease of unknown origin should be considered in the differential diagnosis of pericarditis, with or without pericardial effusion. Cardiac tamponade is a very rare sequela that requires an invasive approach, such as percutaneous or surgical pericardial drainage, in addition to the usual conservative therapy. The authors describe a case of adult-onset Still's disease rendered more difficult by pericarditis and cardiac tamponade, and they briefly review the literature on this entity.
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