Cryptogenic Multifocal Ulcerous Stenosing Enteritis (CMUSE): A Tale of Three Decades | Zendy

Ayaskanta Singh | Zendy; Manoj Kumar Sahu | Zendy; Manas Kumar Panigrahi | Zendy; Debasis Misra | Zendy

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Cryptogenic Multifocal Ulcerous Stenosing Enteritis (CMUSE): A Tale of Three Decades

Author(s) -

Ayaskanta Singh,

Manoj Kumar Sahu,

Manas Kumar Panigrahi,

Debasis Misra

Publication year - 2017

Publication title -

acg case reports journal

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 0.112

H-Index - 4

ISSN - 2326-3253

DOI - 10.14309/crj.2017.44

Subject(s) - medicine , enteritis , intestinal pseudo obstruction , ileus , melena , stenosis , pathogenesis , gastroenterology , pathology , radiology

We present a patient who, over the course of 35 years, presented with repeated episodes of ileus and melena and was misdiagnosed several times, leading to several surgeries. Macroscopic and microscopic features of his resected intestine were compatible with cryptogenic multifocal ulcerous stenosis enteritis (CMUSE), but additional angioectatic lesions were also noted. The patient responded dramatically to hormonal therapy consisting of ethinylestradiol and norethisterone. To our knowledge, this is the first reported case of CMUSE that has shown response to hormonal therapy. We suggest that this is a variant of CMUSE in which vasculopathy plays a role in the pathogenesis.

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