MACRODYSTROPHIA LIPOMATOSA: A CASE REPORT WITH REVIEW OF LITERATURE

Macrodystrophia Lipomatosa is a rare cause of congenital macrodactyly which is characterised by progressive proliferation of all mesenchymal elements, with a disproportionate increase in fibroadipose tissue. [1] It presents as a localised gigantism of hand or foot. This developmental anomaly is reportedly more common in foot than in hand, with a predilection for the plantar and median nerve distribution. Clinical diagnosis is possible with the help of radiography or magnetic resonance imaging(MRI). There are many clinical conditions with similar presentation but imaging and histopathology can lead to confirmatory diagnosis. The treatment option is surgical excision preferably cosmetic surgery.