Development and Treatment of Tertiary Hyperparathyroidism in Patients with Pseudohypoparathyroidism Type 1B
Author(s) -
Nicola M. Neary,
Diala ElMaouche,
Rachel Hopkins,
Steven K. Libutti,
Arnold M. Moses,
Lee S. Weinstein
Publication year - 2012
Publication title -
the journal of clinical endocrinology and metabolism
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.206
H-Index - 353
eISSN - 1945-7197
pISSN - 0021-972X
DOI - 10.1210/jc.2012-1655
Subject(s) - pseudohypoparathyroidism , tertiary hyperparathyroidism , medicine , hyperparathyroidism , pediatrics , endocrinology , parathyroid hormone , parathyroidectomy , calcium
Pseudohypoparathyroidism type 1B (PHP1B) patients have PTH resistance at the renal proximal tubule and develop hypocalcemia and secondary hyperparathyroidism. Hyperparathyroid bone disease also develops in some patients. PHP1B patients are at theoretical risk of developing tertiary hyperparathyroidism.
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