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Pirfenidone in idiopathic pulmonary fibrosis: real-life experience in the referral centre of Siena
Author(s) -
Lucia Vietri,
Paolo Cameli,
Marco Perruzza,
Behar Cekorja,
Laura Bergantini,
Miriana d’Alessandro,
Rosa Metella Refini,
Maria Pieroni,
Antonella Fossi,
David Bennett,
Marco Spalletti,
Maria Antonietta Mazzei,
Piersante Sestini,
Paola Rottoli,
Elena Bargagli
Publication year - 2020
Publication title -
therapeutic advances in respiratory disease
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.022
H-Index - 37
eISSN - 1753-4666
pISSN - 1753-4658
DOI - 10.1177/1753466620906326
Subject(s) - pirfenidone , medicine , idiopathic pulmonary fibrosis , vital capacity , adverse effect , interstitial lung disease , pulmonary function testing , surgery , discontinuation , lung , diffusing capacity , lung function
Our findings confirm the efficacy of pirfenidone in reducing functional progression of IPF and its excellent safety profile in a real-life setting. This study, designed on a long-term follow up, contributes to the growing evidence on safety, tolerability and efficacy of pirfenidone in IPF.

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