Open AccessCochlear Implantation in X‐linked Mixed Deafness
Author(s) -
Prickett Kara K.,
Todd Norman W.
Publication year - 2012
Publication title -
otolaryngology–head and neck surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.232
H-Index - 121
eISSN - 1097-6817
pISSN - 0194-5998
DOI - 10.1177/0194599812451426a331
Subject(s) - medicine , cochlear implantation , perioperative , audiology , cochlear implant , cochlea , active listening , rehabilitation , incidence (geometry) , surgery , psychology , physical therapy , physics , communication , optics
Objective 1) Describe important points of consideration when planning cochlear implant surgery for patients at risk for cerebrospinal fluid (CSF) gusher on cochleostomy. 2) Report successful cochlear implantation in patients with X‐linked mixed deafness. Method Fraternal twins with X‐linked mixed deafness were enrolled in an observational study at a tertiary academic medical center from 2010 to 2011. Subjects underwent cochlear implantation and were followed during recovery and auditory rehabilitation. Main outcome measures included successful placement of electrode arrays into the cochlea, adequate control of leaking CSF, incidence of postoperative complications, and development of listening and speaking communication skills in children with implants. Results Electrode arrays were successfully placed despite challenging middle and inner ear abnormalities. Leaking CSF was controlled without the use of lumbar drains. No perioperative or postoperative complications occurred. Both patients progressed rapidly in the development of hearing, listening, and speaking skills after successful cochlear implantation. A new surgical instrument was designed and used to aid in electrode insertion into gushing CSF. Conclusion Cochlear implantation in patients with X‐linked mixed deafness requires careful planning and execution, but may result in excellent communicative outcomes.