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Mortality and Sudden Death in Pediatric Left Ventricular Noncompaction in a Tertiary Referral Center
Author(s) -
Samuel T. Brescia,
Joseph W. Rossano,
Ricardo Pignatelli,
John L. Jefferies,
Jack F. Price,
Jamie A. Decker,
Susan W. Denfield,
William J. Dreyer,
O’Brian Smith,
Jeffrey A. Towbin,
Jeffrey J. Kim
Publication year - 2013
Publication title -
circulation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 7.795
H-Index - 607
eISSN - 1524-4539
pISSN - 0009-7322
DOI - 10.1161/circulationaha.113.002511
Subject(s) - medicine , cardiology , left ventricular noncompaction , sudden cardiac death , hazard ratio , ventricular tachycardia , cardiomyopathy , sudden death , ventricle , myocardial infarction , ventricular fibrillation , heart failure , confidence interval
Left ventricular noncompaction is a cardiomyopathy characterized by excessive trabeculation of the left ventricle, progressive myocardial dysfunction, and early mortality. Left ventricular noncompaction has a heterogeneous clinical presentation that includes arrhythmia and sudden cardiac death.

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