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Quantitative Myocardial Perfusion in Fabry Disease
Author(s) -
Kristopher Knott,
João B. Augusto,
Sabriordin,
Rebecca Kozor,
Claudia Camaioni,
Hui Xue,
Rebecca Hughes,
Charlotte Manisty,
Louise Brown,
Peter Kellman,
Uma Ramaswami,
Derralynn Hughes,
Sven Plein,
James Moon
Publication year - 2019
Publication title -
circulation cardiovascular imaging
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.584
H-Index - 99
eISSN - 1942-0080
pISSN - 1941-9651
DOI - 10.1161/circimaging.119.008872
Subject(s) - perfusion , medicine , cardiology , fibrosis , magnetic resonance imaging , left ventricular hypertrophy , edema , ejection fraction , muscle hypertrophy , endocardium , radiology , heart failure , blood pressure
FD patients have reduced perfusion, particularly in the subendocardium with greater reductions with LVH, storage, edema, and scar. Perfusion is reduced even without LVH suggesting it is an early disease marker.

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