Open AccessValvular heart disease in four patients with Maroteaux-Lamy syndrome.
Author(s) -
C.T. Tan,
Hartzell V. Schaff,
Fletcher A. Miller,
W. D. Edwards,
Pamela S. Karnes
Publication year - 1992
Publication title -
circulation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 7.795
H-Index - 607
eISSN - 1524-4539
pISSN - 0009-7322
DOI - 10.1161/01.cir.85.1.188
Subject(s) - medicine , disease , valvular heart disease , cardiology
Maroteaux-Lamy syndrome is a lysosomal storage disease of mucopolysaccharide metabolism (MPS type VI) that may involve the mitral and aortic valves. Affected patients have other skeletal and oropharyngeal malformations that complicate anesthetic and surgical management.
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