Gaucher's Disease of the Lung Causing Severe Pulmonary Hypertension with Associated Acute Recurrent Pericarditis
Author(s) -
William C. Roberts,
Donald S. Fredrickson
Publication year - 1967
Publication title -
circulation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 7.795
H-Index - 607
eISSN - 1524-4539
pISSN - 0009-7322
DOI - 10.1161/01.cir.35.4.783
Subject(s) - medicine , hemopericardium , pulmonary hypertension , cardiac tamponade , etiology , gaucher's disease , pathological , pericarditis , acute pericarditis , lung , disease , pericardial effusion , cardiology , pathology
The clinical and pathological features of a 30-year-old man with Gaucher's disease are described. He had severe pulmonary hypertension resulting from obstruction of pulmonary capillaries by Gaucher cells. Acute recurrent pericarditis of unknown etiology terminally led to hemopericardium and cardiac tamponade.
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