Partial Anomalous Pulmonary Venous Drainage with Intact Interatrial Septum Associated with Congenital Mitral Stenosis

A case of partial anomalous pulmonary venous drainage with intact interatrial septum associated with mitral stenosis is reported. The roentgenogram showed plethora confined to the anomalously draining lung tissue, i.e., right upper amd middle lobes, and when the patient developed pulmonary edema, rales were confined to normally draining lung tissue, i.e., left lung and right lower lobe.The pulmonary capillary “wedge” pressures recorded from the normally draining lung tissue reflected the left atrial hypertension, while “wedge” pressures recorded from anomalously draining lung tissue were much lower and reflected the right atrial pressure. Left heart catheterization confirmed the presence of mitral stenosis. Autopsy examination revealed congenital mitral and aortic stenosis, anomalous venous drainage from the right upper and middle lobes and an intact interatrial septum. The differential pulmonary plethora, the differential pulmonary edema, and the differential pulmonary capillary wedge pressures suggested the correct diagnosis during life.