Endocardial Cushion Defect with Pulmonic Stenosis

Five patients with endocardial cushion defect, pulmonic stenosis, and right-to-left shunt have been presented. Valvular pulmonic stenosis was present in all, with additional infundibular stenosis in two. Four patients had complete atrioventricular canal defects. In two children both great arteries arose from the right ventricle. In the clinical differentiation of this entity from the common forms of cyanotic congenital heart disease, the electrocardiogram, characterized by left axis deviation and a counterclockwise inscription of the plane vector loop, is the most helpful tool. The surgical problems presented may be formidable and even impossible to solve, if both great arteries emerge from the right ventricle.