Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor in an Adolescent with Neurofibromatosis Type 1 | Zendy

Jong Hyung Yoon | Zendy; HyunSung Lee | Zendy; Jong In Chun | Zendy; Seog-Yun Park | Zendy; Hyeon Jin Park | Zendy; ByungKiu Park | Zendy

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Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor in an Adolescent with Neurofibromatosis Type 1

Author(s) -

Jong Hyung Yoon,

HyunSung Lee,

Jong In Chun,

Seog-Yun Park,

Hyeon Jin Park,

ByungKiu Park

Publication year - 2014

Publication title -

case reports in pediatrics

Language(s) - English

Resource type - Journals

eISSN - 2090-6803

pISSN - 2090-6811

DOI - 10.1155/2014/951252

Subject(s) - medicine , neurofibromatosis , malignant peripheral nerve sheath tumor , malignancy , head and neck , girl , soft tissue , neurofibromatosis type i , nerve sheath neoplasm , surgery , radiology , pathology , psychology , developmental psychology

Malignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue malignancy usually found in patients with neurofibromatosis type 1 (NF1) with a poor outcome. Although MPNST can be found in any part of the body including head and neck or extremities, intrathoracic MPNST with or without NF1 is uncommon, especially in children or adolescents. Reported herein is a case of huge intrathoracic MPNST in a 16-year-old girl with NF1, and a brief review of the literature.

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