Primary Systemic Amyloidosis and High Levels of Angiotensin-Converting Enzyme: Two Case Reports
Author(s) -
Julia PraenaSegovia,
Amparo Sánchez-Gastaldo,
Máximo Bernabéu-Wittel,
Rafael Felix Ocete-Perez,
R. Ávila-Polo,
Maria Luisa Martino
Publication year - 2013
Publication title -
case reports in cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.106
H-Index - 5
eISSN - 2090-6412
pISSN - 2090-6404
DOI - 10.1155/2013/976379
Subject(s) - amyloidosis , medicine , sarcoidosis , angiotensin converting enzyme , systemic disease , primary systemic amyloidosis , heart failure , cardiology , pathology , disease , blood pressure
Infiltrative heart diseases are caused by a heterogeneous group of disorders; amyloidosis and sarcoidosis are two frequent causes of myocardial infiltration, which differ in clinical and biological outcome and treatment issues. The presence of high levels of angiotensin-converting enzyme (ACE) in a patient with infiltrative heart disease may increase suspicion of sarcoidosis. Nevertheless, no mention about increased ACE levels in extracerebral primary systemic amyloidosis is available. We present two cases of primary systemic amyloidosis, which are cardiac involvement and elevated ACE levels.
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