Acute Pancreatitis with Rapid Clinical Improvement in a Child with Isovaleric Acidemia | Zendy

Elpis Mantadakis | Zendy; Ioannis Chrysafis | Zendy; Emmanouela Tsouvala | Zendy; Athanasios Evangeliou | Zendy; Αthanassios Chatzimichael | Zendy

AI Assistant Blog Pricing

Home ZAIA Blog

Open Access

Acute Pancreatitis with Rapid Clinical Improvement in a Child with Isovaleric Acidemia

Author(s) -

Elpis Mantadakis,

Ioannis Chrysafis,

Emmanouela Tsouvala,

Athanasios Evangeliou,

Αthanassios Chatzimichael

Publication year - 2013

Publication title -

case reports in pediatrics

Language(s) - English

Resource type - Journals

eISSN - 2090-6803

pISSN - 2090-6811

DOI - 10.1155/2013/721871

Subject(s) - medicine , abdominal pain , pancreatitis , acute pancreatitis , vomiting , context (archaeology) , differential diagnosis , propionic acidemia , gastroenterology , pathology , paleontology , biology

Isovaleric acidemia is a rare branched-chain organic acidemia. The authors describe a 3.5-year-old girl with isovaleric acidemia and acute abdominal pain associated with bilious emesis. Elevated serum amylase and abdominal ultrasonography demonstrating an enlarged and edematous pancreas, along with the presence of peripancreatic exudates, confirmed the presence of acute pancreatitis. The patient recovered quickly with intravenous hydration, pancreatic rest, and administration of intravenous L-carnitine. Pancreatitis should be ruled out in the context of vomiting in any patient with isovaleric acidemia. Conversely, branched-chain organic acidemias should be included in the differential diagnosis of any child with pancreatitis of unknown origin.

The content you want is available to Zendy users.

Already have an account? Click here to sign in.

Having issues? You can contact us here

Accelerating Research