Malignant Peripheral Nerve Sheath Tumor of the Small Bowel: An Unusual Presentation with Fatal Outcome
Author(s) -
Amina Mohtaram,
Siham Mesmoudi,
Hind Mrabti,
Amal Rami,
Rachida Latib,
Z. Bernoussi,
Imane Aaribi,
Meryam Ben Ameur El Youbi,
Hassan Errihani
Publication year - 2013
Publication title -
case reports in oncological medicine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.173
H-Index - 7
eISSN - 2090-6714
pISSN - 2090-6706
DOI - 10.1155/2013/423867
Subject(s) - medicine , malignant peripheral nerve sheath tumor , perforation , lesion , presentation (obstetrics) , leiomyosarcoma , peripheral nerve , peripheral , sarcoma , soft tissue , fibrosarcoma , surgery , nerve sheath , pathology , schwannoma , anatomy , immunohistochemistry , materials science , punching , metallurgy
Malignant peripheral nerve sheath tumor of the small bowel is an extremely rare disease. Histologic distinction from other types of soft tissue sarcoma especially fibrosarcoma and leiomyosarcoma requires electron microscopy. Complete surgery remains the only curative treatment. However, late diagnosis makes curative surgery more difficult. The contribution of chemotherapy to incomplete surgery has been proved without controlled studies. We report a case of this type of lesion discovered following a small bowel perforation.
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