Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
Author(s) -
Matteo Fassan,
Mauro Cassaro,
Massimo Vecchiato,
Roberto Clemente,
Gianmaria Pennelli,
Stefano Merigliano,
Giuseppe Altavilla
Publication year - 2012
Publication title -
case reports in pathology
Language(s) - English
Resource type - Journals
eISSN - 2090-6781
pISSN - 2090-679X
DOI - 10.1155/2012/438505
Subject(s) - perivascular epithelioid cell , esophagus , dysphagia , pathology , lesion , medicine , epithelioid cell , gastrointestinal tract , smooth muscle , immunohistochemistry , anatomy , radiology
Malignant perivascular epithelioid cell tumor (PEComa) is a rare tumor composed of hybrid tumor cells characterized by immunoreactivity for both melanocytic and smooth muscle markers. This paper describes the uncommon esophageal location of an 8 cm PEComa in a 75-year-old Caucasian man who was presented with ingravescent dysphagia. Although PEComas arising within the gastrointestinal tract are exceptional findings, clinicians should not exclude this class of tumors in the diagnostic investigation of a bulky lesion of the esophageal wall.
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