Primary Malignant Fibrous Histiocytoma: A Rare Case
Author(s) -
Anastasios Katsourakis,
George Noussios,
Iosif Hadjis,
Neofitos Evangelou,
Efthimios Chatzitheoklitos
Publication year - 2011
Publication title -
case reports in medicine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.2
H-Index - 20
eISSN - 1687-9627
pISSN - 1687-9635
DOI - 10.1155/2011/134801
Subject(s) - medicine , gemcitabine , rare disease , natural history , adjuvant chemotherapy , sarcoma , jejunum , myalgia , trunk , chemotherapy , neoplasm , surgery , disease , pathology , cancer , ecology , breast cancer , biology
Malignant fibrous histiocytoma (MFH) of the small intestine is an extremely rare condition. It occurs most commonly in the extremities and the trunk. We report a case of a 67-year-old woman who admitted with fever, myalgia, and altered status. After thorough investigation, a tumor of the jejunum was found. The patient underwent complete surgical removal of the tumor. A diagnosis of MFN (undifferentiated high-grade pleomorphic sarcoma) was made. The patient received adjuvant chemotherapy with Gemcitabine. Two years after the operation, the patient died due to recurrence of the disease. MFH of the small intestine is an extremely rare neoplasm with an aggressive biological behaviour. In this paper, pathogenesis, natural history, and treatment are reviewed.
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