Polyarteritis Nodosa and Bronchiolitis Obliterans with Organizing Pneumonia, an Unusual Association
Author(s) -
Kaberi Dasgupta,
Andrew Watters,
A. Zidulka
Publication year - 1997
Publication title -
canadian respiratory journal
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.675
H-Index - 53
eISSN - 1916-7245
pISSN - 1198-2241
DOI - 10.1155/1997/717581
Subject(s) - medicine , bronchiolitis obliterans organizing pneumonia , polyarteritis nodosa , bronchiolitis obliterans , vasculitis , pneumonia , cryptogenic organizing pneumonia , systemic vasculitis , dermatology , pathology , lung , disease , lung transplantation
Bronchiolitis obliterans and organizing pneumonia (BOOP) is an inflammatory, fibrotic disorder of the small airways, alveoli and pulmonary intersitium. Often idiopathic and usually benign, this condition may cause dyspnea and influenza-like symptoms. Polyarteritis nodosa (PAN) is a small and medium vessel vasculitis, which usually involves the kidney and other viscera but rarely results in vasculitis of the lungs. This is the second case of BOOP associated with PAN reported in the literature. Knowledge of this association is likely to be of value because an undiagnosed vasculitis can rapidly become fatal
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