Amyloid myopathy presenting with respiratory failure. | Zendy

John R. Ashe | Zendy; Cecil O. Borel | Zendy; G Hart | Zendy; Richard L. Humphrey | Zendy; D A Derrick | Zendy; Ralph W. Kuncl | Zendy

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Amyloid myopathy presenting with respiratory failure.

Author(s) -

John R. Ashe,

Cecil O. Borel,

G Hart,

Richard L. Humphrey,

D A Derrick,

Ralph W. Kuncl

Publication year - 1992

Publication title -

journal of neurology neurosurgery and psychiatry

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 3.391

H-Index - 206

eISSN - 1468-330X

pISSN - 0022-3050

DOI - 10.1136/jnnp.55.2.162

Subject(s) - macroglossia , myopathy , medicine , pathology , respiratory failure , amyloidosis , pathological , diaphragm (acoustics) , infiltration (hvac) , muscle biopsy , weakness , amyloid (mycology) , respiratory system , biopsy , anatomy , tongue , physics , acoustics , loudspeaker , thermodynamics

Amyloidosis is a rare cause of myopathy. Its prominent or presenting feature may be respiratory failure. Physiological measurement of transdiaphragmatic pressure and biopsy specimens of muscle show the pathological mechanism to be diaphragm weakness due to amyloid infiltration of the diaphragm rather than parenchymal lung involvement. Thus amyloid myopathy even without the typical macroglossia and muscle pseudohypertrophy should be considered as one of the neurological causes of respiratory failure.

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